Publication:
Successful treatment of a child with Schwartz-Jampel syndrome using rapid maxillary expansion and CPAP

dc.contributor.authorPeanchitlertkajorn S.
dc.contributor.authorAssawakawintip T.
dc.contributor.authorPibulniyom M.
dc.contributor.authorSrisan P.
dc.contributor.authorPungchanchaikul P.
dc.contributor.authorJaroenying R.
dc.date.accessioned2022-03-10T13:16:53Z
dc.date.available2022-03-10T13:16:53Z
dc.date.issued2021
dc.date.issuedBE2564
dc.description.abstractStudy Objectives:We reported an 8-year-old male patient with Schwartz-Jampel syndrome, severe obstructive sleep apnea, constricted maxilla and moderate tonsillar hypertrophy. The syndrome is characterized by myotonia, skeletal dysplasia, and facial dysmorphism. Methods: CPAP was initially prescribed, but he was not able to tolerate due to a high pressure setting. Rapid maxillary expansion alone reduced AHI to 10.4 events/h. Results: When combined with CPAP, AHI is further reduced to 2.4 events/h. The patient has a better compliance with CPAP following rapid maxillary expansion therapy as the pressure setting decreased. Conclusions: This is the first report utilizing a combination of rapid maxillary expansion and CPAP therapy to successfully treat severe pediatric OSA. © 2021 American Academy of Sleep Medicine. All rights reserved.
dc.format.mimetypeapplication/pdf
dc.identifier.citationJournal of Clinical Sleep Medicine. Vol 17, No.3 (2021), p.601-604
dc.identifier.doi10.5664/jcsm.9028
dc.identifier.issn15509389
dc.identifier.other2-s2.0-85102537434
dc.identifier.urihttps://hdl.handle.net/20.500.14740/7864
dc.language.isoeng
dc.rights.holderScopus
dc.subject.otherAdenotonsillar hypertrophy
dc.subject.otherArticle
dc.subject.otherBone dysplasia
dc.subject.otherCase report
dc.subject.otherChild
dc.subject.otherClinical article
dc.subject.otherContinuous positive airway pressure
dc.subject.otherFace dysmorphia
dc.subject.otherHuman
dc.subject.otherHypertrophy
dc.subject.otherMale
dc.subject.otherMaxilla
dc.subject.otherMyotonia
dc.subject.otherOrthodontic procedure
dc.subject.otherPalatal expansion
dc.subject.otherPanoramic radiography
dc.subject.otherPatient compliance
dc.subject.otherPolysomnography
dc.subject.otherSchool child
dc.subject.otherSchwartz Jampel syndrome
dc.subject.otherSleep disordered breathing
dc.subject.otherTreatment outcome
dc.subject.otherChondrodysplasia
dc.subject.otherMaxilla
dc.subject.otherPalatal expansion
dc.subject.otherPositive end expiratory pressure ventilation
dc.subject.otherSleep disordered breathing
dc.subject.otherChild
dc.subject.otherContinuous Positive Airway Pressure
dc.subject.otherHumans
dc.subject.otherMale
dc.subject.otherMaxilla
dc.subject.otherOsteochondrodysplasias
dc.subject.otherPalatal Expansion Technique
dc.subject.otherPatient Compliance
dc.subject.otherSleep Apnea, Obstructive
dc.titleSuccessful treatment of a child with Schwartz-Jampel syndrome using rapid maxillary expansion and CPAP
dc.typeArticle
dspace.entity.typePublication
swu.datasource.scopushttps://www.scopus.com/inward/record.uri?eid=2-s2.0-85102537434&doi=10.5664%2fjcsm.9028&partnerID=40&md5=00865e950a906d9c72fe6bc79e6f6265

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