Publication:
Successful treatment of a child with Schwartz-Jampel syndrome using rapid maxillary expansion and CPAP

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Issued Date

2021

Resource Type

Article

Language

eng

File Type

application/pdf

ISSN

15509389

DOI

10.5664/jcsm.9028

Other identifier(s)

2-s2.0-85102537434

Rights Holder(s)

Scopus

Bibliographic Citation

Journal of Clinical Sleep Medicine. Vol 17, No.3 (2021), p.601-604

Suggested Citation

Peanchitlertkajorn S., Assawakawintip T., Pibulniyom M., Srisan P., Pungchanchaikul P., Jaroenying R. Successful treatment of a child with Schwartz-Jampel syndrome using rapid maxillary expansion and CPAP. Journal of Clinical Sleep Medicine. Vol 17, No.3 (2021), p.601-604. doi:10.5664/jcsm.9028 Retrieved from: https://hdl.handle.net/20.500.14740/7864

Title

Successful treatment of a child with Schwartz-Jampel syndrome using rapid maxillary expansion and CPAP

Author(s)

Peanchitlertkajorn S.
 Assawakawintip T.
 Pibulniyom M.
 Srisan P.
 Pungchanchaikul P.
 Jaroenying R.

Abstract

Study Objectives:We reported an 8-year-old male patient with Schwartz-Jampel syndrome, severe obstructive sleep apnea, constricted maxilla and moderate tonsillar hypertrophy. The syndrome is characterized by myotonia, skeletal dysplasia, and facial dysmorphism. Methods: CPAP was initially prescribed, but he was not able to tolerate due to a high pressure setting. Rapid maxillary expansion alone reduced AHI to 10.4 events/h. Results: When combined with CPAP, AHI is further reduced to 2.4 events/h. The patient has a better compliance with CPAP following rapid maxillary expansion therapy as the pressure setting decreased. Conclusions: This is the first report utilizing a combination of rapid maxillary expansion and CPAP therapy to successfully treat severe pediatric OSA. © 2021 American Academy of Sleep Medicine. All rights reserved.

Subject(s)

Adenotonsillar hypertrophy
 Article
 Bone dysplasia
 Case report
 Child
 Clinical article
 Continuous positive airway pressure
 Face dysmorphia
 Human
 Hypertrophy
 Male
 Maxilla
 Myotonia
 Orthodontic procedure
 Palatal expansion
 Panoramic radiography
 Patient compliance
 Polysomnography
 School child
 Schwartz Jampel syndrome
 Sleep disordered breathing
 Treatment outcome
 Chondrodysplasia
 Maxilla
 Palatal expansion
 Positive end expiratory pressure ventilation
 Sleep disordered breathing
 Child
 Continuous Positive Airway Pressure
 Humans
 Male
 Maxilla
 Osteochondrodysplasias
 Palatal Expansion Technique
 Patient Compliance
 Sleep Apnea, Obstructive

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URI

https://hdl.handle.net/20.500.14740/7864

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Scopus: Year 1983-2021

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