Publication: Cutis Marmorata Telangiectatica Congenita: Clinical Features in 7 Cases
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Issued Date
2016
Resource Type
File Type
application/pdf
ISSN
1252208
Other identifier(s)
2-s2.0-85049386926
Rights Holder(s)
Scopus
Bibliographic Citation
Journal of the Medical Association of Thailand = Chotmaihet thangphaet. Vol 99, (2016), p.S227-S230
Suggested Citation
Wirotpaisankul P., Wannaprasert T., Treesirichod A. Cutis Marmorata Telangiectatica Congenita: Clinical Features in 7 Cases. Journal of the Medical Association of Thailand = Chotmaihet thangphaet. Vol 99, (2016), p.S227-S230. Retrieved from: https://hdl.handle.net/20.500.14740/4961
Author(s)
Abstract
Cutis marmorata telangiectatica congenita (CMTC) is a sporadic congenital vascular anomaly usually presents at birth as a localized or generalized reticulated, erythema and telangiectasia. The pathogenesis of CMTC is unknown. Additional anomalies have been frequently reported in association with CMTC. This article describes the characteristics of the clinical presentations in a series of 7 children with CMTC in HRH Princess Maha Chakri Sirindhorn Medical Center, Srinakharinwirot University, Thailand. Both genders were almost equally affected (3 male/4 female). The lower limbs were involved in 7 patients (100%), the trunk in 3 patients (42.9%), and the upper limbs in 1 patient (14.3%). There were 2 patients (28.6%) who presented with the involvement of both trunk and limbs. The mean of the body surface area involved was 17% (2-50). Asymmetry of affected limbs were found in 2 patients (28.6%). On follow-up, improvement of reticulated lesions was noted in all patients. The prognosis of uncomplicated cases is good. No specific treatment is needed. The skin lesions usually disappear gradually.