Please use this identifier to cite or link to this item: https://ir.swu.ac.th/jspui/handle/123456789/17338
Title: Successful treatment of a child with Schwartz-Jampel syndrome using rapid maxillary expansion and CPAP
Authors: Peanchitlertkajorn S.
Assawakawintip T.
Pibulniyom M.
Srisan P.
Pungchanchaikul P.
Jaroenying R.
Keywords: adenotonsillar hypertrophy
Article
bone dysplasia
case report
child
clinical article
continuous positive airway pressure
face dysmorphia
human
hypertrophy
male
maxilla
myotonia
orthodontic procedure
palatal expansion
panoramic radiography
patient compliance
polysomnography
school child
Schwartz Jampel syndrome
sleep disordered breathing
treatment outcome
chondrodysplasia
maxilla
palatal expansion
positive end expiratory pressure ventilation
sleep disordered breathing
Child
Continuous Positive Airway Pressure
Humans
Male
Maxilla
Osteochondrodysplasias
Palatal Expansion Technique
Patient Compliance
Sleep Apnea, Obstructive
Issue Date: 2021
Abstract: Study Objectives:We reported an 8-year-old male patient with Schwartz-Jampel syndrome, severe obstructive sleep apnea, constricted maxilla and moderate tonsillar hypertrophy. The syndrome is characterized by myotonia, skeletal dysplasia, and facial dysmorphism. Methods: CPAP was initially prescribed, but he was not able to tolerate due to a high pressure setting. Rapid maxillary expansion alone reduced AHI to 10.4 events/h. Results: When combined with CPAP, AHI is further reduced to 2.4 events/h. The patient has a better compliance with CPAP following rapid maxillary expansion therapy as the pressure setting decreased. Conclusions: This is the first report utilizing a combination of rapid maxillary expansion and CPAP therapy to successfully treat severe pediatric OSA. © 2021 American Academy of Sleep Medicine. All rights reserved.
URI: https://ir.swu.ac.th/jspui/handle/123456789/17338
https://www.scopus.com/inward/record.uri?eid=2-s2.0-85102537434&doi=10.5664%2fjcsm.9028&partnerID=40&md5=00865e950a906d9c72fe6bc79e6f6265
ISSN: 15509389
Appears in Collections:Scopus 1983-2021

Files in This Item:
There are no files associated with this item.


Items in SWU repository are protected by copyright, with all rights reserved, unless otherwise indicated.