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Title: | Successful treatment of a child with Schwartz-Jampel syndrome using rapid maxillary expansion and CPAP |
Authors: | Peanchitlertkajorn S. Assawakawintip T. Pibulniyom M. Srisan P. Pungchanchaikul P. Jaroenying R. |
Keywords: | adenotonsillar hypertrophy Article bone dysplasia case report child clinical article continuous positive airway pressure face dysmorphia human hypertrophy male maxilla myotonia orthodontic procedure palatal expansion panoramic radiography patient compliance polysomnography school child Schwartz Jampel syndrome sleep disordered breathing treatment outcome chondrodysplasia maxilla palatal expansion positive end expiratory pressure ventilation sleep disordered breathing Child Continuous Positive Airway Pressure Humans Male Maxilla Osteochondrodysplasias Palatal Expansion Technique Patient Compliance Sleep Apnea, Obstructive |
Issue Date: | 2021 |
Abstract: | Study Objectives:We reported an 8-year-old male patient with Schwartz-Jampel syndrome, severe obstructive sleep apnea, constricted maxilla and moderate tonsillar hypertrophy. The syndrome is characterized by myotonia, skeletal dysplasia, and facial dysmorphism. Methods: CPAP was initially prescribed, but he was not able to tolerate due to a high pressure setting. Rapid maxillary expansion alone reduced AHI to 10.4 events/h. Results: When combined with CPAP, AHI is further reduced to 2.4 events/h. The patient has a better compliance with CPAP following rapid maxillary expansion therapy as the pressure setting decreased. Conclusions: This is the first report utilizing a combination of rapid maxillary expansion and CPAP therapy to successfully treat severe pediatric OSA. © 2021 American Academy of Sleep Medicine. All rights reserved. |
URI: | https://ir.swu.ac.th/jspui/handle/123456789/17338 https://www.scopus.com/inward/record.uri?eid=2-s2.0-85102537434&doi=10.5664%2fjcsm.9028&partnerID=40&md5=00865e950a906d9c72fe6bc79e6f6265 |
ISSN: | 15509389 |
Appears in Collections: | Scopus 1983-2021 |
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