Please use this identifier to cite or link to this item: https://ir.swu.ac.th/jspui/handle/123456789/15221
ชื่อเรื่อง: The ultrastructural study in a case of Fabry disease
ผู้แต่ง: Palungwachira P.
Yaguchi H.
Keywords: adult
article
case report
Fabry disease
human
male
pathology
skin
ultrastructure
Adult
Fabry Disease
Humans
Male
Skin
วันที่เผยแพร่: 2002
บทคัดย่อ: An investigation of the ultrastructural study was conducted on specimens from a typical patient with Fabry disease. Numerous characteristic cytoplasmic inclusions were observed in the vascular endothelial cell, pericyte, smooth muscle cell, nerve and eccrine sweat glands, the lamellar pattern of which were considerably variable in various types of gland cells. Large vacuolar inclusions predominated in clear cells of the secretory coil; lesser vacuoles were also seen in the coiled duct, and the basal cells of the straight duct toward the coiled duct displayed mulberry-like figures. There were some clear cells showing cell damage and necrosis in the secretory coil. Lamellated bodies were noted in the axons and schwann cells around the eccrine sweat glands. The small blood vessels around the eccrine glands were narrowed by swollen endothelial cells with heavy inclusions. These intracytoplasmic deposits may be responsible for the decreased sweating ability in Fabry disease. The factors related to hypohidrosis are also discussed.
URI: https://ir.swu.ac.th/jspui/handle/123456789/15221
https://www.scopus.com/inward/record.uri?eid=2-s2.0-0036653875&partnerID=40&md5=02f53eb8d05aee75cd73b5b0e985c88f
ISSN: 1252208
Appears in Collections:Scopus 1983-2021

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